It a birth defect where in part of small brain i.e. cerebellum sags down causing pressure on the brain stem resulting in collection of water inside spinal cord which is known as syrinx.
It usually presents with progressive pulsatile headache to begin with and then gradually leads to imbalance and weakness in both hands.
Chiari malformation 1
36 yrs lady presented with neck pain and right hand weakness.
MRI Neck showed Chiari 1 malformation causing Cervico-dorsal syrinx.
Underwent formen magnum decompression
